Multicentric Infantile Myofibromatosis
نویسنده
چکیده
We present a case of multicentric infantile myofibromatosis in a 3-month-old male infant who had multiple papular lesions on his extremities and trunk and a slowly growing and bulging mass on his left occipital area since birth. His general physical condition was good and psychomotor development was normal. The diagnosis was established by histopathological and immunohistochemical studies along with clinical manifestations and imaging findings. The patient underwent left occipital craniectomy and the defect was repaired with bone cement. He had been doing well with spontaneous regression of one of the skin lesions on his face 6 months after the operation. (Dermatol Sinica 24: 47-51, 2006)
منابع مشابه
Congenital Infantile Myofibromatosis: A Case Report and Review of Literature
Received March 29, 2003 Abstract Congenital infantile myofibromatosis is a rare disorder with multiple fibromatous tumours in skin, bone, muscle, viscera and subcutaneous tissue presenting in early infancy. Multiple lytic bone lesions and vertebra involvement are also common, mimicking the clinical picture of metastatic tumours. However, it is a disease with variable prognosis depending on the ...
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